Carotid rete mirabile in pseudoxanthoma elasticum, just a coincidence ?

A pediatric case of carotid rete mirabile.

BACKGROUND Carotid rete mirabile (CRM) is a physiological network between the external carotid and internal carotid systems in lower mammals. Very rarely, these arterial channels are observed in humans. CASE DESCRIPTION We describe a 13-year-old girl with CRM who presented with acute hemiplegia after an operation for Dieulafoy's ulcer, a submucosal vascular anomaly of the stomach. Angiogram r...

Carotid rete mirabile associated with subarachnoid hemorrhage.

A 47-year-old man presented with carotid rete mirabile manifesting as subarachnoid hemorrhage (SAH). Computed tomography showed SAH, and angiography disclosed an abnormal vascular network around the petrous and cavernous portions of the internal carotid artery. Single photon emission computed tomography (SPECT) with technetium-99m methyl cysteinate dimer revealed reduced regional cerebral blood...

Case Reports A Pediatric Case of Carotid Rete Mirabile

Background Carotid rete mirabile (CRM) is a physiological network between the external carotid and internal carotid systems in lower mammals. Very rarely, these arterial channels are observed in humans. Case Description We describe a 13-year-old girl with CRM who presented with acute hemiplegia after an operation for Dieulafoy's ulcer, a submucosal vascular anomaly of the stomach. Angiogram rev...

Pseudoxanthoma elasticum

Pseudoxanthoma elasticum (PXE) is a genetic metabolic disease with autosomal recessive inheritance caused by mutations in the ABCC6 gene. The lack of functional ABCC6 protein leads to ectopic mineralization that is most apparent in the elastic tissues of the skin, eyes and blood vessels. The clinical prevalence of PXE has been estimated at between 1 per 100,000 and 1 per 25,000, with slight fem...

Pseudoxanthoma elasticum